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Volume 3 Issue 5 November (Supplement) 2015

Case Reports

AN UNUSUAL PRESENTATION OF A RARE DISORDER - SCLEREDEMA OF BUSCHKE
Sreela L S, Sharma R N, Sudheesh M

Scleredema, also known as Buschke disease (scleredema of Buschke) or scleredema adultorum is a rare connective tissue disorder characterized by progressive thickening and hardening of the skin, usually on the areas of the face, upper back, neck and shoulders. This self-limiting skin disorder is usually associated with conditions like long standing diabetes mellitus with poor glycemic control, recent streptococcal upper respiratory tract infection or paraprotenemia. The pathophysiology of scleredema and its relationship with these associated disorders are not clearly understood. Few therapeutic options are proposed without satisfying results. We report an unusual case of scleredema in a 47-year-old woman who presented with indurated edema of the face, neck and abdomen in the absence of other associated medical conditions.  
Key words: Scleredema, Buschke, adultorum.

 
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