Crouzon syndrome is a rare inherited autosomal dominant genetic disorder affecting first branchial arch that causes craniofacial dysmorphy by affecting growth and development of cranium and facial skeletons. Disease process starts from in utero and continues to develop to 2 to 3 years of age. Crouzons child usually presents with various clinical manifestations. On severe course, Crouzon’s Syndrome may cause difficulties in breathing, feeding, vision and brain development. Management of Crouzons child should be undertaken with multi-disciplinary coordinated clinical team care that involves surgical treatment based on cosmetics and severity of child needs. This review article highlights the importance of clinical manifestations, disease frequency, diagnosis, treatment protocal of multidisciplinary approach required for the management of this craniofacial dysostosis that favours early detection and prognosis of syndrome child.
Key words: Crouzons syndrome, craniosynostosis.