The most common birth defect is the presence of a cleft and 27-34.3% of the clefts in the face are those found only in the palate. The prevalence of ICP varies from 0.17 to 0.7 out of 1000 live births. Females are equally or more affected by a ratio of 1.5-1.6/1 than males. Pierre Robin sequence is a congenital anomaly characterized by micrognathia, cleft palate and glossoptosis at varying levels and presentations. It could be seen as an isolated anomaly or be associated with other congenital conditions or one feature of many syndromes. Several methods have been described in the management of PRS. The main aim of treatment focused at respiratory distress and nutrition. Extreme vigilance is required during every stage of the management of anomalies presented with PRS. Efficient palatoplasty is required to treat the cleft in palatal region so that patient regains the level of proper nutrition and speech in a smooth and speedily manner.
Keywords: Palatoplasty, Pierre Robin sequence, retrognathic mandible.